Double-outlet right ventricle associated with persistent common atriventricular canal.

Double-outlet Right Ventricle Associated with Persistent Common Atrioventricular Canal

A variant of double-outlet right ventricle (DORV) associated with common atrioventricular (A-V) canal was identified. As yet, this syndrome has not been successfully repaired. Of 16 patients with this diagnosis, 14 had the diagnosis confirmed at postmortem examination and two had the diagnosis confirmed by exploratory cardiotomy. The 16 patients were divided into two groups according to the pos...

Double outlet right ventricle associated with persistent common atrioventricular canal and pulmonary stenosis.

A case of a month-old baby admitted for dyspnea and cyanosis, is described. His past history consisted of only mild cyanosis during crying. On physical examination nail beds and lips were cyanotic; on heart auscultation the pulmonary second sound was single. The chest X-ray showed a decreased pulmonary vascularity; the ECG demonstrated extreme right axis deviation (-170 degrees). Capillary gas ...

Double outlet right ventricle.

double-outlet right ventricle

In a previous study the possibility that tetralogy of Fallot and transposition of the great arteries may arise as a result of embryonic arrests in the normal rotation of the junction of the outflow tract and the great arteries was investigated. The results suggested that the development of other transposition complexes such as double-outlet right ventricle might also be related to arrests in th...

Absence of pulmonic valve associated with double-outlet right ventricle.

ABSENCE of the pulmonic valve is a rare congenital lesion which is usually associated with tetralogy of Fallot." 2 We have recently observed a patient in whom this anomaly coexisted with "double-outlet right ventricle." This case is reported because a review of the literature has failed to reveal a similar case and because certain difficulties inherent in the differentiation of double-outlet ri...